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North Star Ambulatory Assessment (NSAA)
Availability
Publicly available: North Star Ambulatory Assessment.
For further information contact: Muscular Dystrophy, UK
Classification
Supplemental – Highly Recommended: Congenital Muscular Dystrophy (CMD) studies with ambulatory CMD patients.
 
Supplemental: Duchenne Muscular Dystrophy/Becker Muscular Dystrophy (DMD/BMD) and Spinal Muscular Atrophy (SMA)
Short Description of Instrument
The North Star Ambulatory Assessment has been developed by the Physiotherapy Assessment and Evaluation Group of the North Star Clinical Network for the assessment of ambulant boys with Duchenne muscular dystrophy (DMD).
Test details and instructions for the patient and a scoring sheet with details for grading should be used in conjunction with each other.
 
Specific Construct Measured: Motor abilities - proximal and axial muscle strength
Comments/Special Instructions
17 tasks activities with progressive difficulty
Each task is given a score from 0–2; max score 34.
Total score of 0 is completely non-ambulant; 34 able to complete all tasks fully
Activities are graded in the following manner:
2 – ‘Normal’ – no obvious modification of activity
1 – Modified method but achieves goal independent of physical assistance from another
0 – Unable to achieve independently
 
Administration: If administered by a trained clinical evaluator, test takes approximately 10–15 min to administer
Equipment
15cm high box step, height appropriate chair/height adjustable plinth, stopwatch, 10m marked ‘runway’
 
General test instructions
If you think that the child is capable of a better performance, it is acceptable to ask the child to repeat the item and re-score if appropriate. You should attempt all activities at each assessment
Do not use a mat unless it is required to gain co-operation. If a mat must be used, make sure it is not heavily padded. Note in comments and do so for all subsequent evaluations
Please note that for many of the items socks and shoes should not be worn
For the timed tests – rise from floor and 10m ‘run’ - please note the time in seconds and only to the nearest tenth of a second
Rise from floor Components of Gowers’ manoeuvre:
Turns towards the floor (into a four-point kneeling position or rolls to prone) Places hands on the floor to assist rising and walks hands back in towards him Uses one or both arms to push up on legs to achieve upright standing
Large base of support by abducting hips and extending knees
Rationale/Justification
Validated only in DMD boys >3y of age
 
Limitations for CMD:
Will not be able to use in non-ambulatory patients
Focuses somewhat on whether or not patient is toe walking
No data in typically developing children.
 
Advantages in CMD:
Tests proximal and axial muscle strength
References
Mazzone ES, Messina S, Vasco G, Main M, Eagle M, D'Amico A, . . . Mercuri E. Reliability of the North Star Ambulatory Assessment in a multicentric setting. Neuromuscul Disord. 2009; 19(7), 458–461.
 
Mazzone E, Martinelli D, Berardinelli A, Messina S, D'Amico A, Vasco G, . . . Mercuri E. North Star Ambulatory Assessment, 6-minute walk test and timed items in ambulant boys with Duchenne muscular dystrophy. Neuromuscul Disord. 2010; 20(11), 712?716.
 
Mazzone E, Vasco G, Sormani MP, Torrente Y, Berardinelli, A, Messina S, . . . Mercuri E. Functional changes in Duchenne muscular dystrophy: a 12- month longitudinal cohort study. Neurology. 2011; 77(3), 250–256.
 
Scott E, Eagle M, Mayhew A, Freeman J, Main M, Sheehan J., . . . Muntoni F. Development of a functional assessment scale for ambulatory boys with Duchenne muscular dystrophy. Physiother Res Int. 2012; 17(2), 101–109.
 
De Sanctis R, Pane M, Sivo S, Ricotti V, Baranello G, Frosini S, . . . Mercuri E. Suitability of North Star Ambulatory Assessment in young boys with Duchenne muscular dystrophy. Neuromuscul Disord. 2015; 25(1), 14–18.
 
Eagle M, Scott E, Main M, Sheehan J, Michelle M, Guglieri M, Straub V, Bushby K. Steroids in Duchenne muscular dystrophy (DMD): Natural history and clinical evaluation using the North Star Ambulatory Assessment (NSAA). Poster presented at the World Muscle Society Conference, Sicily. Abstract in Neuromuscul Disord. 2007; 17(9–10): 774
 
Ergul Y, Ekici B, Nisli K, Tatli B, Binboga F, Acar G, . . . Omeroglu RE. Evaluation of the North Star Ambulatory Assessment scale and cardiac abnormalities in ambulant boys with Duchenne muscular dystrophy. J Paediatr Child Health 2012; 48(7), 610–616.
 
Mayhew A, Cano S, Scott E, Eagle M, Bushby K,& Muntoni F. Moving towards meaningful measurement: Rasch analysis of the North Star Ambulatory Assessment in Duchenne muscular dystrophy. Dev Med Child Neurol.  2011; 53(6), 535– 542.
 
Mayhew AG, Cano SJ, Scott E, Eagle M, Bushby K, Manzur A,& Muntoni F. Detecting meaningful change using the North Star Ambulatory Assessment in Duchenne muscular dystrophy. Dev Med Child Neurol. 2013; 55(11), 1046–1052.
 
Scott E, Eagle M, Main M, Sheehan, J. The North Star Ambulatory Assessment. Poster presented at the Annual Meeting of the British Paediatric Neurology Association, 2006. Abstract in Dev Med Child Neurol 2006; 48(Supp. 104): 27.
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