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CDE Detailed Report
This report contains detailed information about the selected CDEs.
Note: If at least one CDE was selected from a copyright- or trademark-protected instrument/scale then all of the CDEs from that instrument/scale are included in this report.
Disease: Friedreich's Ataxia
Sub-Domain: Ataxia and Performance Measures
CRF: Friedreich's Ataxia Rating Scale (FARS)
Item count: 90 (90 distinct CDEs)
CDE ID
CDE Name
Variable Name
Definition / Description
Question Text
Permissible Value
Description
Data Type
Instructions
References
Population
Classification (e.g., Core)
Version #
Version Date
Aliases for Variable Name
CRF Module / Guideline
© or TM
Sub-Domain
Domain
Previous Title
Size
Input Restrictions
Min Value
Max Value
Measurement Type
LOINC ID
SNOMED
caDSR ID
CDISC ID
C11738
Friedreich's Ataxia Rating Scale (FARS) - functional staging ataxia score
FARSFunctnlStageAtaxScore
Functional staging for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Functional staging for ataxia: Stage
0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;
Stage 0: Normal;;Stage 1.0: Minimal signs detected by physician during screening. Can run or jump without loss of balance. No disability;;Stage 2.0: Symptoms present, recognized by patient, but still mild. Cannot run or jump without losing balance. The patient is physically capable of leading an independent life, but daily activities may be somewhat restricted. Minimal disability;;Stage 3.0: Symptoms are overt and significant. Requires regular or periodic holding onto wall/furniture or use of a cane for stability and walking. Mild disability. (Note: many patients postpone obtaining a cane by avoiding open spaces and walking with the aid of walls/people etc. These patients are graded as stage 3.0);;Stage 4.0: Walking requires a walker, Canadian crutches or two canes, or other aids such as walking dogs. Can perform several activities of daily living. Moderate disability;;Stage 5.0: Confined but can navigate a wheelchair. Can perform some activities of daily living that do not require standing or walking. Severe disability;;Stage 6.0: Confined to wheelchair or bed with total dependency for all activities of daily living. Total disability;
Numeric Values
Increments of 0.5 may be used if the status is about the middle between two stages.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Exploratory
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q1
 
Single Pre-Defined Value Selected
       
C11739
Friedreich's Ataxia Rating Scale (FARS) - daily activities speech score
FARSDailyActivsSpeechScore
Speech score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Speech
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Mildly affected. No difficulty being understood;;2 - Moderately affected. Sometimes asked to repeat statements;;3 - Severely affected. Frequently asked to repeat statements;;4 - Unintelligible most of the time;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.1
 
Single Pre-Defined Value Selected
       
C11740
Friedreich's Ataxia Rating Scale (FARS) - daily activities swallowing score
FARSDailyActivsSwallowScore
Swallowing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Swallowing
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Rare choking (< once a month);;2 - Frequent choking (< once a week, > once a month);;3 - Requires modified food, chokes multiple times a week, or patient avoids certain foods;;4 - Requires NG tube or gastrostomy feedings;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.2
 
Single Pre-Defined Value Selected
       
C11741
Friedreich's Ataxia Rating Scale (FARS) - daily activities cutting handling utensils score
FARSDalyActsCutUtensilScore
Cutting-food-and-handling-utensils score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Cutting Food and Handling Utensils
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Somewhat slow and clumsy, but no help needed;;2 - Clumsy and slow but can cut most foods with some help needed, or needs assistance when in a hurry;;3 - Food must be cut by someone, but can still feed self slowly;;4 - Needs to be fed;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.3
 
Single Pre-Defined Value Selected
       
C11742
Friedreich's Ataxia Rating Scale (FARS) - daily activities dressing score
FARSDailyActivsDressingScore
Dressing score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Dressing
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Somewhat slow, but no help needed;;2 - Occasional assistance with buttoning, getting arms in sleeves, etc., or has to modify activity in some way (e.g., having to sit to get dressed, use velcro for shoes, stop wearing ties, etc.);;3 - Considerable help required, but can do some things alone;;4 - Helpless;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.4
 
Single Pre-Defined Value Selected
       
C11743
Friedreich's Ataxia Rating Scale (FARS) - daily activities personal hygiene score
FARSDailyActivsPrsnlHygnScore
Personal hygiene score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Personal Hygiene
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Somewhat slow, but no help needed;;2 - Very slow hygienic care or has need for devices such as special grab bars, tub bench, shower chair, etc.;;3 - Requires personal help with washing, brushing teeth, combing hair or using toilet;;4 - Fully dependent;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.5
 
Single Pre-Defined Value Selected
       
C11744
Friedreich's Ataxia Rating Scale (FARS) - daily activities falling score
FARSDailyActivsFallingScore
Falling score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Falling
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Rare falling (< once a month);;2 - Occasional falls (once a week to once a month);;3 - Falls multiple times a week or requires device to prevent falls;;4 - Unable to stand or walk;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. Assistive device = score 3.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.6
 
Single Pre-Defined Value Selected
       
C11745
Friedreich's Ataxia Rating Scale (FARS) - daily activities walking score
FARSDailyActivsWalkingScore
Walking score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Walking
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Mild difficulty, perception of imbalance;;2 - Moderate difficulty, but requires little or no assistance;;3 - Severe disturbance of walking, requires assistance or walking aids;;4 - Cannot walk at all even with assistance (wheelchair bound);
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. Assistive device = score 3.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.7
 
Single Pre-Defined Value Selected
       
C11746
Friedreich's Ataxia Rating Scale (FARS) - daily activities sitting position quality score
FARSDailyActivsSitQualtyScore
Quality-of-sitting-position score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Quality of Sitting Position
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Slight imbalance of the trunk, but needs no back support;;2 - Unable to sit without back support;;3 - Can sit only with extensive support (Geriatric chair, posy, etc.);;4 - Unable to sit;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.8
 
Single Pre-Defined Value Selected
       
C11747
Friedreich's Ataxia Rating Scale (FARS) - daily activities bladder function score
FARSDailyActivsBladrFuncScore
Bladder function score for ataxia in subject/participant, as part of the Friedreich's Ataxia Rating Scale (FARS).
Bladder Function
0;0.5;1;1.5;2;2.5;3;3.5;4;
0 - Normal;;1 - Mild urinary hesitance, urgency or retention (< once a month);;2 - Moderate hesitance, urgency, rare retention/incontinence (> once a month, but < once a week);;3 - Frequent urinary incontinence (> once a week);;4 - Loss of bladder function requiring intermittent catheterization/indwelling catheter;
Numeric Values
Increments of 0.5 may be used if strongly felt that a task falls between 2 scores. If using drugs for bladder, automatic score of 3.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2.9
 
Single Pre-Defined Value Selected
       
C11748
Friedreich's Ataxia Rating Scale (FARS) - daily activities total value
FARSDailyActivtyTotalVal
The sum of the scores recorded for Part 2: Activities of Daily Living section, as part of the Friedreich's Ataxia Rating Scale (FARS).
Total Activities of Daily Living Score:
0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;11.5;12;12.5;13;13.5;14;14.5;15;15.5;16;16.5;17;17.5;18;18.5;19;19.5;20;20.5;21;21.5;22;22.5;23;23.5;24;24.5;25;25.5;26;26.5;27;27.5;28;28.5;29;29.5;30;30.5;31;31.5;32;32.5;33;33.5;34;34.5;35;35.5;36;
0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;11.5;12;12.5;13;13.5;14;14.5;15;15.5;16;16.5;17;17.5;18;18.5;19;19.5;20;20.5;21;21.5;22;22.5;23;23.5;24;24.5;25;25.5;26;26.5;27;27.5;28;28.5;29;29.5;30;30.5;31;31.5;32;32.5;33;33.5;34;34.5;35;35.5;36;
Numeric Values
Enter numeric value for score of 0-36. Refer to instructions on form.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q2 Total activities of daily living score
 
Single Pre-Defined Value Selected
       
C11749
Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar facial atrophy fasciculation myoclonus weakness score
FARSNEBulbrFacAtrFasMyWeaScore
The score for severity of facial atrophy, fasciculation, action myoclonus, and weakness in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Facial Atrophy, Fasciculation, Action Myoclonus, and Weakness:
0;0.5;1;1.5;2;2.5;3;
0 - None;;1 - Fasciculations or action myoclonus, but no atrophy;;2 - Atrophy present but not profound or complete;;3 - Profound atrophy and weakness;
Numeric Values
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3A.1
 
Single Pre-Defined Value Selected
       
C11750
Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar tongue atrophy fasciculation myoclonus weakness score
FARSNEBulbrTonAtroFasMyWeScore
The score for severity of tongue atrophy, fasciculation, action myoclonus, and weakness in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Tongue Atrophy, Fasciculation, Action Myoclonus and Weakness:
0;0.5;1;1.5;2;2.5;3;
0 - None;;1 - Fasciculations or action myoclonus, but no atrophy;;2 - Atrophy present but not profound or complete;;3 - Profound atrophy and weakness;
Numeric Values
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3A.2
 
Single Pre-Defined Value Selected
       
C11751
Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar cough score
FARSNeuroBulbrCoughScore
The score for forcefulness of cough in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Cough
0;0.5;1;1.5;2;
0 - Normal;;1 - Depressed;;2 - Totally or nearly absent;
Numeric Values
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities. Patient asked to cough forcefully 3 times.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3A.3
 
Single Pre-Defined Value Selected
       
C11752
Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar spontaneous speech score
FARSNeuroBulbrSpontSpeechScore
The score for understandability of spontaneous speech in the bulbar portion of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Spontaneous Speech
0;0.5;1;1.5;2;2.5;3;
0 - Normal;;1 - Mild (all or most words understandable);;2 - Moderate (most words not understandable);;3 - Severe (no or almost no useful speech);
Numeric Values
Rate each item on the basis of the patient status during examination. To the extent possible, sequential patient examinations should be carried out at the same time of the day. If the patient is taking any medication, the examination should be carried out prior to dosing, or at a fixed time following the dosing based on the maximum expected therapeutic response. Increments of 0.5 may be used if examiner feels an item falls between 2 defined severities. Ask the patient to read or repeat the sentences "The President lives in the White House" or "The traffic is heavy today".
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3A.4
 
Single Pre-Defined Value Selected
       
C11753
Friedreich's Ataxia Rating Scale (FARS) - neurological exam bulbar total value
FARSNeuroBulbrTotalVal
The sum of the scores recorded for Part 3: Neurological Examination A. Bulbar, as part of the Friedreich's Ataxia Rating Scale (FARS).
Total Bulbar Score
0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;
0;0.5;1;1.5;2;2.5;3;3.5;4;4.5;5;5.5;6;6.5;7;7.5;8;8.5;9;9.5;10;10.5;11;
Numeric Values
Enter number value of 0-11. Refer to instructions on form.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3A Total bulbar score
 
Single Pre-Defined Value Selected
       
C11754
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger-finger test right score
FARSNeuExULCFingrFingrRtScore
The score for the right finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Finger to Finger Test
0;1;2;3;
0 - Normal;1 - Mild oscillations of finger (< 2 cm);2 - Moderate oscillations of finger (2-6 cm);3 - Severe oscillations of finger (> 6 cm);
Numeric Values
The index fingers are placed in front of each other with flexion at the elbow about 25 cm from the sternum. Observe for 10 seconds. Score amplitude of oscillations:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.1 - right
 
Single Pre-Defined Value Selected
       
C11755
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger-finger test left score
FARSNeuExULCFingrFingrLftScore
The score for the left finger in the finger-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Finger to Finger Test
0;1;2;3;
0 - Normal;1 - Mild oscillations of finger (< 2 cm);2 - Moderate oscillations of finger (2-6 cm);3 - Severe oscillations of finger (> 6 cm);
Numeric Values
The index fingers are placed in front of each other with flexion at the elbow about 25 cm from the sternum. Observe for 10 seconds. Score amplitude of oscillations
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.1 - left
 
Single Pre-Defined Value Selected
       
C11756
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination nose-finger test right score
FARSNeuExULCNoseFingrRtScore
The score for the right finger in the nose-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Nose-Finger Test
0;1;2;3;4;
0 - None;1 - Mild (< 2 cm amplitude);2 - Moderate (2-4 cm amplitude or persisting through movement);3 - Severe (> 6 cm & persisting through movement);4 - Too poorly coordinated to perform task;
Numeric Values
Assess kinetic or intention tremor during and towards the end of movement: examiner holds index finger at 90% reach of patient; test at least 3 nose-finger-nose trials; movement slow > 3 sec.:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.2 - right
 
Single Pre-Defined Value Selected
       
C11757
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination nose-finger test left score
FARSNeuExULCNoseFingrLftScore
The score for the left finger in the nose-to-finger test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Nose-Finger Test
0;1;2;3;4;
0 - None;1 - Mild (< 2 cm amplitude);2 - Moderate (2-4 cm amplitude or persisting through movement);3 - Severe (> 6 cm & persisting through movement);4 - Too poorly coordinated to perform task;
Numeric Values
Assess kinetic or intention tremor during and towards the end of movement: examiner holds index finger at 90% reach of patient; test at least 3 nose-finger-nose trials; movement slow > 3 sec.:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.2 - left
 
Single Pre-Defined Value Selected
       
C11758
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination dysmetria right score
FARSNeuExULCDysmetriaRtScore
The score for the right finger in the dysmetria (fast nose-finger) test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Dysmetria (Fast Nose-Finger) Test
0;1;2;3;4;
0 - None;1 - Mild (misses 2 or fewer times);2 - Moderate (misses 3-5 times);3 - Severe (misses 6-8 times);4 - Too poorly coordinated to perform task;
Numeric Values
Assess dysmetria: The patient touches tip of examiner’s finger 8 times as rapidly as possible while the examiner moves his finger and stops at different locations at about 90% reach of the patient. Assess dysmetria—i.e., inaccuracy of reaching the target—at examiner’s finger.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.3 - right
 
Single Pre-Defined Value Selected
       
C11759
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination dysmetria left score
FARSNeuExULCDysmetriaLftScore
The score for the left finger in the dysmetria (fast nose-finger) test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Dysmetria (Fast Nose-Finger) Test
0;1;2;3;4;
0 - None;1 - Mild (misses 2 or fewer times);2 - Moderate (misses 3-5 times);3 - Severe (misses 6-8 times);4 - Too poorly coordinated to perform task;
Numeric Values
Assess dysmetria: The patient touches tip of examiner’s finger 8 times as rapidly as possible while the examiner moves his finger and stops at different locations at about 90% reach of the patient. Assess dysmetria—i.e., inaccuracy of reaching the target—at examiner’s finger.
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.3 - left
 
Single Pre-Defined Value Selected
       
C11760
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination rapid alternate hand movement right score
FARSNeuExULCRapdAltHandRtScore
The score for the right hand in the rapid alternating movement of hands test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Rapid Alternating Movements of Hands
0;1;2;3;
0 - Normal;1 - Mild (slightly irregular or slowed);2 - Moderate (irregular and slowed);3 - Too poorly coordinated to perform task.;
Numeric Values
Forearm pronation/supination 15 cm above thigh; 10 full cycles as fast as possible; assess rate, rhythm, accuracy; practice 10 cycles before rating, if time > 7 sec add 1 to score. Use stopwatch:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.4 - right
 
Single Pre-Defined Value Selected
       
C11761
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination rapid alternate hand movement left score
FARSNeuExULCAltHandLftScore
The score for the left hand in the rapid alternating movement of hands test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Rapid Alternating Movements of Hands
0;1;2;3;
0 - Normal;1 - Mild (slightly irregular or slowed);2 - Moderate (irregular and slowed);3 - Too poorly coordinated to perform task.;
Numeric Values
Forearm pronation/supination 15 cm above thigh; 10 full cycles as fast as possible; assess rate, rhythm, accuracy; practice 10 cycles before rating, if time > 7 sec add 1 to score. Use stopwatch:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.4 - left
 
Single Pre-Defined Value Selected
       
C11762
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger taps right score
FARSNeuExULCFingerTapsRtScore
The score for the right hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Finger Taps
0;1;2;3;4;
Normal;Mild (misses 1-3 times);Moderate (misses 4-9 times);Severe (misses 10-15 times);Cannot perform the task.;
Numeric Values
Index-fingertip to thumb-crease; 15 reps as fast as possible; practice 15 reps once before rating; if time > 6 sec, add 1 to rating. Use stopwatch:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.5 - right
 
Single Pre-Defined Value Selected
       
C11763
Friedreich's Ataxia Rating Scale (FARS) - neurological exam upper limb coordination finger taps left score
FARSNeuExULCFingerTapsLftScore
The score for the left hand in the finger taps test in the upper limb coordination section of the neurological exam, as part of the Friedreich's Ataxia Rating Scale (FARS).
Finger Taps
0;1;2;3;4;
Normal;Mild (misses 1-3 times);Moderate (misses 4-9 times);Severe (misses 10-15 times);Cannot perform the task.;
Numeric Values
Index-fingertip to thumb-crease; 15 reps as fast as possible; practice 15 reps once before rating; if time > 6 sec, add 1 to rating. Use stopwatch:
Subramony SH, May W, Lynch D, et al. (2005). Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology. 64:1261-2. Delatycki MB. (2009). Evaluating the progression of Friedreich ataxia and its treatment. J Neurol. 2009. 256(Suppl 1):36-41.
Adult;Pediatric
Core
3.0
7/11/2013
Aliases for variable name not defined
Friedreich's Ataxia Rating Scale (FARS)
Ataxia and Performance Measures
Outcomes and End Points
FARS Q3B.5 - left
 
Single Pre-Defined Value Selected
       
07-20-2019
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